A case report, Management of a Gelzmen's disease in surgery of hemorrhagic ovarian cyst

Author
fatemeh Emampour
Department of Anesthesiology, School of Medicine, Cardiovascular Diseases Research Center, Birjand University of Medical Sciences,Birjand,Iran
Abstract
Introduction

Glanzmann's thrombasthenia is the hereditary disease of abnormal function in the platelets. Despite being rare, this disease Given the direct relationship between the rate of cousin marriages and the disease prevalence. The main problem in the treatment of the disease is performing particularly major surgeries. In the present case report, we stated case management of the hemorrhagic ovarian cyst with a history of Gelzmen's disease.

Case report

With a history of Gelzmen's disease, the adolescent girl presented with a pain in the abdominal area. After performing ultrasound and taking a medical history and the related tests conducted, the patient was diagnosed with a hemorrhagic ovarian cyst. Before the surgery, the patient received three vials of the recombinant activated factor VII. During and after the operation, she was received three vials in every two hours, and three vials every six hours until homeostasis. Finally, the patient was discharged four days later with the satisfactory general condition

Conclusion

Concerning the previous studies as well as our experience, we could manage the patient bleeding during and after the surgery for treatment of the hemorrhagic ovarian cyst by preoperative injections of the platelets and the factor VII during and after the operation
Keywords
Glanzman
Surgery
ovarian cyst
platelet
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